Abstract
Introduction: Dextrocardia is rare in the general population and may be associated with significant additional cardiac malformations. It is commonly associated with additional cardiac malformations.
In this report, we have described the follow-up of a patient with Situs inversus dextrocardia and cyanotic complex cardiopathy in a 16-year-old Albanian male. The male patient, born in 2007 in Albania, was referred to our ambulatory at 6 months of life by a pediatrician cause of cyanosis and cardiac murmur. It was performed the echo Color Doppler examination, with the conclusion: situs inversus dextrocardia, unique ventricle, pulmonary arterial atresia. In 2008, a diagnostic catheterization was performed. The medico-chirurgical consultation has decided to leave the boy in natural history with a periodic follow–up. On 06.2009, in one of the routine examinations, there was evidence of hypertrophy of the unique ventricle associated with arterial hypertension. From that time, the patient is under medical treatment with periodic monitoring.
Conclusions: Regular follow-up of complex cyanogen congenital heart disease enhances healthcare for a high-risk target group. In a heave desaturations patient, the hypertension must be evaluated as a secondary complication of the primary problem.
References
Perloff JK, Marelli AJ. Perloff’s Clinical Recognition of Congenital Heart Disease, 6th Edition, Philadelphia, PA: Saunders: Elsevier; 2012, 15–30.]
Casey B. Two rights make a wrong: human left-right malformations. Human Molecular Genetics 1998;1565–71. https://doi.org/10.1093/hmg/7.10.1565
Maldjian PD, Saric M. Approach to Dextrocardia in Adults: Review. AJR 2007;188:S39–49. https://doi.org/10.2214/AJR.06.1179
Solzbach, U., Beuter, M., Hartig, B. et al. Isolated Dextrocardia with Situs Solitus (Dextroversion). Herz 35, 207–210 (2010). https://doi.org/10.1007/s00059-010-3279-5
Buxton A, Morganroth J, Josephson M, Perloff J, Shelburne J. Isolated dextroversion of the heart with asymmetric septal hypertrophy. Am. Heart Journal 1976; 92:785–90. https://doi.org/10.1016/S0002-8703(76)80017–8.
Bohun CM, Potts JE, Casey BM, et al. A population-based study of cardiac malformations and outcomes associated with dextrocardia. Am J Cardiol. 2007;100(2):305-309. PMID: 17631088. doi: 10.1016/ j.amjcard.2007.02.095.
Leung AK, Robson WL. Dextrocardia with Situs [corrected] solitus. CMAJ. 2006 Aug 1;175(3):244. PMID: 16880440; PMCID: PMC1513419. doi: 10.1503/cmaj.060721. Erratum in: CMAJ. 2006;175(6):624.

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